The third and last of the staged congenital heart surgeries performed to treat hypoplastic left heart syndrome (HLHS) and other single ventricle heart defects is the Fontan procedure. It is usually performed between the ages of 18 months and three years.
About the Fontan Procedure
During a Fontan procedure, congenital heart surgeons reroute the blood flow from the lower body to the lungs by connecting the inferior vena cava to the pulmonary artery. To accomplish this, surgeons will most often create a connecting channel, or tube, outside of the heart. Blood flow from the lower body now joins the connection made in the second, Glenn, procedure, in which the blood flow from the upper body was rerouted to the lungs. Once the blood is oxygen-enriched in the lungs, the heart's single, right ventricle drives it out to the body again.
Since the Fontan procedure requires open heart surgery, your toddler will be on a heart-lung machine to temporarily take over blood circulation and breathing. The procedure will last about five hours. Recovery from Fontan surgery usually requires a two- or three-week hospital stay that will start in the cardiac intensive care unit (CICU). Learn more about postoperative care following surgeries for hypoplastic left heart syndrome.
Outstanding Fontan procedure outcomes
Children undergoing Fontan surgery are older and at less risk than when they were newborns facing open heart surgery, so survival rates are generally high – especially at Children's Hospital of Wisconsin, where they exceed 99 percent. Congenital heart surgeons at Children's are among the few in the nation board certified in congenital heart surgery. Our congenital heart surgery program is 3-star rated by the Society of Thoracic Surgeons, the highest rating they grant. See our overall pediatric congenital surgery outcomes.
Fontan Survivorship and Advanced Therapies Program
Our Fontan Survivorship Program was created specifically to care for children, adolescents, and adults with single ventricle heart disease, such as hypoplastic left heart syndrome. Although survival and outcomes after the Fontan procedure have improved, some patients may develop health problems later in life. These “Fontan-associated” problems may impact not just the heart, but also other parts of the body such as the lungs, gastrointestinal system, liver, growth, and other aspects of the child’s health and development. Our Fontan Survivorship Program is staffed by a multidisciplinary team of experts trained to provide the best possible care for children and adults who have had the Fontan procedure.